Mediastinal fibrosis is inherited in an autosomal recessive manner
Specialty
Pulmonology
Causes
histoplasmosis
Treatment
glucocorticoids or immunosuppressants[1]
Mediastinal fibrosis is characterized by invasive, calcified fibrosis centered on lymph nodes that block major vessels and airways. In Europe, this disease is exceptionally rare. More cases are seen in USA where the disease may often be associated with histoplasmosis.[2][3]
^Rossi, Giovanni M.; Emmi, Giacomo; Corradi, Domenico; Urban, Maria L.; Maritati, Federica; Landini, Federica; Galli, Paola; Palmisano, Alessandra; Vaglio, Augusto (June 2017). "Idiopathic Mediastinal Fibrosis: a Systemic Immune-Mediated Disorder. A Case Series and a Review of the Literature". Clinical Reviews in Allergy & Immunology. 52 (3): 446–459. doi:10.1007/s12016-016-8584-1. PMID 27553003. S2CID 46747661.
^Davis AM, Pierson RN, Loyd JE (2001). "Mediastinal fibrosis". Seminars in Respiratory Infections. 16 (2): 119–30. doi:10.1053/srin.2001.24242. PMID 11521244.
^Mitchell IM, Saunders NR, Maher O, Lennox SC, Walker DR (1986). "Surgical treatment of idiopathic mediastinal fibrosis: report of five cases". Thorax. 41 (3): 210–4. doi:10.1136/thx.41.3.210. PMC 460296. PMID 3715778.
and 25 Related for: Mediastinal fibrosis information
Mediastinalfibrosis is characterized by invasive, calcified fibrosis centered on lymph nodes that block major vessels and airways. In Europe, this disease...
this is called scarring, and if fibrosis arises from a single cell line, this is called a fibroma. Physiologically, fibrosis acts to deposit connective tissue...
Mediastinal lymphadenopathy or mediastinal adenopathy is an enlargement of the mediastinal lymph nodes. There are many possible causes of mediastinal...
1595. The name "cystic fibrosis" refers to the characteristic fibrosis and cysts that form within the pancreas. Cystic fibrosis typically manifests early...
sound in idiopathic pulmonary fibrosis velcro crackles on auscultation in a person with idiopathic pulmonary fibrosis Problems playing this file? See...
idiopathic pulmonary fibrosis and other fibrotic lung diseases. Despite extensive investigation, the cause of IPF remains unknown. The fibrosis in IPF has been...
disease eventually develop pulmonary fibrosis which has a median survival of 2.5-3.5 years. Idiopathic pulmonary fibrosis is interstitial lung disease for...
variety of sites. Known manifestations include retroperitoneal fibrosis, mediastinalfibrosis and Riedel's thyroiditis. They are now considered to be manifestations...
fibrosis) and nodules, scarring within the chest cavity (mediastinalfibrosis) or in the anatomic space behind the abdomen (retroperitoneal fibrosis)...
Pneumomediastinum (from Greek pneuma – "air", also known as mediastinal emphysema) is pneumatosis (abnormal presence of air or other gas) in the mediastinum...
esophagus or the pericardium. A particularly dangerous condition is mediastinalfibrosis, in which a subset of individuals with granulomatous mediastinitis...
Bauxite fibrosis is a progressive form of pneumoconiosis usually caused by occupational exposure to bauxite fumes which contain aluminium and silica particulates...
cystic fibrosis. Cystic fibrosis eventually results in severe bronchiectasis in nearly all cases. The cause in 10–50% of those without cystic fibrosis is...
mediastinitis is due to a granulomatous process of the mediastinal lymph nodes leading to fibrosis and chronic abscesses in the mediastinum. The most common...
(pleural fibrosis), or some cancers (tumors within the bronchi, lung, or pleural cavity) and certain lymphomas associated with the mediastinal lymph nodes...
thoracic cavity on each side of the mediastinum, and can be subdivided into mediastinal (covering the lateral surfaces of the fibrous pericardium, oesophagus...
bronchopulmonary aspergillosis in patients with cystic fibrosis: HLA and ABPA in cystic fibrosis". Microbiology and Immunology. 57 (3): 193–197. doi:10...
opioid withdrawal accompanied by lacrimation. Other causes include cystic fibrosis, whooping cough, nasal tumors, hormonal changes, and cluster headaches...
the chronic forms of interstitial pneumonia such as idiopathic pulmonary fibrosis. The most common symptoms of acute interstitial pneumonitis are highly...
infection. Recurrent episodes are more likely in persons with asthma, cystic fibrosis, and poor immune function. In early stages an ENT doctor confirms sinusitis...
ash dust, lead particles, pollen grains etc) has caused interstitial fibrosis. The three most common types are asbestosis, silicosis, and coal miner's...
though it is unclear exactly how this results in fibrosis. The precise mechanisms producing the fibrosis are not entirely clear. However, research indicates...
Global Information