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Dentin dysplasia information


Dentin dysplasia
Preoperative panoramic radiographs showing features of dentin dysplasia type I
SpecialtyDentistry

Dentin dysplasia (DD) is a rare genetic developmental disorder affecting dentine production of the teeth, commonly exhibiting an autosomal dominant inheritance that causes malformation of the root. It affects both primary and permanent dentitions in approximately 1 in every 100,000 patients.[1] It is characterized by the presence of normal enamel but atypical dentin with abnormal pulpal morphology. Witkop[1] in 1972 classified DD into two types which are Type I (DD-1) is the radicular type, and type II (DD-2) is the coronal type. DD-1 has been further divided into 4 different subtypes (DD-1a,1b,1c,1d) based on the radiographic features.[2]

  1. ^ a b Kim, J.-W.; Simmer, J.P. (2007-05-01). "Hereditary Dentin Defects". Journal of Dental Research. 86 (5): 392–399. doi:10.1177/154405910708600502. ISSN 0022-0345. PMID 17452557. S2CID 1279513.
  2. ^ Shields, E.D.; Bixler, D.; El-Kafrawy, A.M. (1973). "A proposed classification for heritable human dentine defects with a description of a new entity". Archives of Oral Biology. 18 (4): 543–IN7. doi:10.1016/0003-9969(73)90075-7. PMID 4516067.

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