Colloidal iron staining shows deposition of glycosaminoglycans in the cornea
Specialty
Ophthalmology
Macular corneal dystrophy, also known as Fehr corneal dystrophy, is a rare pathological condition affecting the stroma of cornea first described by Arthur Groenouw in 1890.[1] Signs are usually noticed in the first decade of life and progress afterwards, with opacities developing in the cornea and attacks of pain. This gradual opacification leads to visual impairment often requiring keratoplasty in the later decades of life.[2]
^Groenouw A. Knötchenförmige Hornhauttrübungen (noduli corneae). Arch Augenheilkunde. 1890;21:281–289.
[citation needed] Corneal stromal dystrophies – Macularcornealdystrophy is manifested by a progressive dense cloudiness of the entire corneal stroma that...
Macularcornealdystrophy, also known as Fehr cornealdystrophy, is a rare pathological condition affecting the stroma of cornea first described by Arthur...
conditions including corneal edema, scars, and macularcornealdystrophy is clinically manifested as corneal opacity. The term corneal blindness is commonly...
Maculardystrophy may refer to any of these eye diseases: Macularcornealdystrophy, a rare pathological condition Macular degeneration, or age-related...
Vitelliform maculardystrophy is an irregular autosomal dominant eye disorder which can cause progressive vision loss. This disorder affects the retina...
Macular degeneration, also known as age-related macular degeneration (AMD or ARMD), is a medical condition which may result in blurred or no vision in...
thought to help maintain optimal corneal hydration; genetic disruption of its synthesis leads to the macularcornealdystrophy. According to one study, average...
infections. Other eye conditions can cause corneal ulcers, such as entropion, distichiasis, cornealdystrophy, and keratoconjunctivitis sicca (dry eye)...
Macular edema occurs when fluid and protein deposits collect on or under the macula of the eye (a yellow central area of the retina) and causes it to...
same guidelines separately divide macular edema into two categories: "macular edema apparently absent" and "macular edema apparently present". The latter...
disease states such as macularcornealdystrophy, in which GAGs levels such as KS are altered, loss of hydration within the corneal stroma is believed to...
disorganised lamellae, leading to thinned and conical-shaped cornea Macularcornealdystrophy, associated with the loss of keratan sulfate Oyster, CW (1999)...
and eye strain. Severe myopia is associated with an increased risk of macular degeneration, retinal detachment, cataracts, and glaucoma. Myopia results...
production of keratan sulfate. Mutations in the gene lead to macularcornealdystrophy. GRCh38: Ensembl release 89: ENSG00000183196 – Ensembl, May 2017...
with corneal astigmatism. A follow-up study in 2013 on the European population, however, found no variant significantly associated with corneal astigmatism...
disease resulted from altered function of UDP-GlcNAc epimerase . Macularcornealdystrophy: is a congenital disease resulted from malfunction of GlcNAc-6-sulfotransferase...
Visual Sciences Archived 13 August 2016 at the Wayback Machine "CornealDystrophies (including Keratoconus)". Eye Info. RNIB. Archived from the original...
clinically based on the signs and symptoms as well as eye examination, but corneal scrapings may be obtained and evaluated using microbiological culture or...
corneal surgery, including penetrating keratoplasty, and understanding of cornealdystrophies and pathologies, such as acute hydrops. "Acute Corneal Hydrops"...
(blepharoconjunctivitis), accompanied by small white itchy lesions on the corneal surface. The effect of the lesions varies, from minor damage to the epithelium...
Epiretinal membrane or macular pucker is a disease of the eye in response to changes in the vitreous humor or more rarely, diabetes. Sometimes, as a result...
known as atrophic age-related macular degeneration (AMD) or advanced dry AMD, is an advanced form of age-related macular degeneration that can result in...