Pulmonary atresia with ventricular septal defect information
Type of congenital heart defect
Medical condition
Pulmonary atresia with ventricular septal defect
Other names
PA-VSDS (abbr.)[1]
A ventricular septal defect, one of the symptoms of this condition, under an ultrasound.
Specialty
Medical genetics
Risk factors
Genetic and environmental factors usually come into place
Diagnostic method
Radiological studies such as chest CT scans.
Differential diagnosis
Pulmonary atresia
Prognosis
poor without treatment
Frequency
rare
Deaths
untreated PAVSD patients more likely to suffer from a premature death
Pulmonary atresia with ventricular septal defect is a rare birth defect characterized by pulmonary valve atresia occurring alongside a defect on the right ventricular outflow tract.[2][3][4][5]
It is a type of congenital heart disease/defect,[6] and one of the two recognized subtypes of pulmonary atresia, the other being pulmonary atresia with intact ventricular septum.[7][8]
^"Pulmonary atresia". Program Operations Manual System (POMS). U.S. Social Security Administration.
^"Pulmonary Atresia: Symptoms, Causes and Treatment". Cleveland Clinic. Retrieved 2022-09-08.
^Cite error: The named reference GARD_PAWVSD was invoked but never defined (see the help page).
case of pulmonaryatresiawithventricularseptaldefect, decreased pulmonary blood flow may cause associated defects such as: Tricuspid atresia Tetralogy...
Pulmonaryatresiawithventricularseptaldefect is a rare birth defect characterized by pulmonary valve atresia occurring alongside a defect on the right...
artery. This can be accomplished by a ventricularseptaldefect (VSD) connecting the left ventricle to the pulmonary artery or by a patent ductus arteriosus...
right ventricle. Pulmonaryatresia is the complete closure of the pulmonary valve. Ebstein's anomaly is the displacement of the septal leaflet of the tricuspid...
helping the body to get oxygen. Pulmonaryatresiawithventricularseptaldefect (or Tetralogy of Fallot withpulmonaryatresia) will result in the development...
malformations: Fallot's tetralogy transposition of the great vessels Ventricular and atrial septaldefects. Deranged abdominal organ asymmetry: The stomach and spleen...
tricuspid atresia, the procedure can be done where the blood does not pass through the morphologic right ventricle; i.e., the systemic and pulmonary circulations...
occurs together with other congenital heart defects, most commonly ventricularseptaldefect and right ventricular outflow tract obstruction. It is sometimes...
or the pulmonary artery. PulmonaryatresiaPulmonary valve stenosis Hypoplastic right heart syndrome Tetralogy of Fallot A left ventricular outflow tract...
Atrial septaldefect: a hole between the right and left upper chambers allows blood from the left to enter the right. Ventricularseptaldefect: a hole...
at all resulting in no possibility of left ventricular output. In the mitral stenosis and aortic atresia (MS-AA) subtype blood is able to fill the left...
father to maintain perfusion while performing a direct repair of a ventricularseptaldefect in a 4-year-old child in 1954. He continued to use cross-circulation...
bicuspid valve. Defects in producing the AV septum produces atrioventricular septaldefects, including a persistent AV canal and tricuspid atresia. The floor...
abnormalities, such as Tetralogy of Fallot, Pulmonary Stenosis, overriding aorta, ventricularseptaldefect, and right ventricular hypertrophy are common amongst Alagille...
(DORV); and Ventricular septaldefect (VSD); and Right ventricular outflow tract obstruction (RVOTO): pulmonaryatresia; or pulmonary stenosis; or subpulmonary...
that surgery can be avoided. Other heart birth defects include ventricularseptaldefect, pulmonaryatresia, and tetralogy of Fallot. An abdominal pregnancy...
venous pressure (CVP) or pulmonary arterial pressure, and specific malformations including unbalanced atrioventricular septaldefect or surgical history of...
stenosis of the aorta and pulmonary trunk, which is a narrowing of the vessels, atrial and/or ventricularseptaldefect, tricuspid atresia, and hypoplastic left...
Global Information