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Ectopia lentis information


Ectopia lentis
Ectopia Lentis in Marfan syndrome. Zonular fibers are being seen.
SpecialtyMedical genetics Edit this on Wikidata
Anterior lens luxation in a dog
Anterior lens luxation with cataract formation in a cat

Ectopia lentis is a displacement or malposition of the eye's crystalline lens from its normal location. A partial dislocation of a lens is termed lens subluxation or subluxated lens; a complete dislocation of a lens is termed lens luxation or luxated lens.

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Ectopia lentis

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Ectopia lentis is a displacement or malposition of the eye's crystalline lens from its normal location. A partial dislocation of a lens is termed lens...

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Hyperhomocysteinemia

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formation. Homocystinuria is the second most common cause of heritable ectopia lentis. Homocystinuria is an autosomal recessive metabolic disorder most often...

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Marfan syndrome

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≥ 2 AND ectopia lentis Aortic root Z-score ≥ 2 AND an FBN1 mutation Aortic root Z-score ≥ 2 AND a systemic score* > 7 points Ectopia lentis AND an FBN1...

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Autosomal recessive isolated ectopia lentis

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Autosomal recessive isolated ectopia lentis is a rare hereditary disorder which is characterized by ectopia lentis (that is; a condition that displaces...

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Photophobia

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epithelium, such as that caused by a corneal foreign body or keratitis Ectopia lentis Endophthalmitis Eye trauma caused by disease, injury, or infection such...

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Corectopia

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normal, central position. It may be associated with high myopia or ectopia lentis, among other conditions. Medical or surgical intervention may be indicated...

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Subluxation

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and other traumas. A subluxation of the lens within the eye is called ectopia lentis, wherein it is displaced or malpositioned. Subluxated lenses are frequently...

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Homocystinuria

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Psychiatric disease Eye anomalies: Ectopia lentis – in contrast to Marfan syndrome which features upward ectopia lentis, downward dislocation is the typical...

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Hyperlysinemia

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α-aminoadipic semialdehyde synthase. Hyperlysinemia is associated with ectopia lentis (a displacement or malposition of the eye's crystalline lens) in humans...

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Astigmatism

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Lens induced glaucomas

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compression of angle by intumescent lens may also cause angle closure. Ectopia lentis is a displacement or malposition of the eye's crystalline lens from...

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Anisocoria

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Scintillating scotoma

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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List of feline diseases

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Diabetes in cats Diaphragmatic hernia Dirofilaria immitis Dry eye syndrome Ectopia lentis Eosinophilic granuloma Fading kitten syndrome, a broad term for neonatal...

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Stye

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Esotropia

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Mydriasis

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Achromatopsia

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Leukocoria

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Norrie disease, ocular toxocariasis, persistence of the tunica vasculosa lentis (PFV/PHPV), retinoblastoma, and retrolental fibroplasia. Because of the...

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Blepharitis

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Oculogyric crisis

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Bitemporal hemianopsia

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Heterochromia iridum

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Miosis

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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Nystagmus

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congenital amaurosis Optic nerve or macular disease Persistent tunica vasculosa lentis Rod monochromatism Visual-motor syndrome of functional monophthalmus Latent...

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Aniridia

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(A); Foveal hypoplasia in proband 27–1 (B); Ptosis, microcornea with dislocated cataractous lens in proband 10–1 (C); Ectopia lentis in proband 16–1 (D)....

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Diplopia

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tunic Lens Cataract Congenital cataract Childhood cataract Aphakia Ectopia lentis Retina Retinitis Chorioretinitis Cytomegalovirus retinitis Retinal detachment...

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