Short QT syndrome (SQT) is a very rare genetic disease of the electrical system of the heart, and is associated with an increased risk of abnormal heart rhythms and sudden cardiac death.[1] The syndrome gets its name from a characteristic feature seen on an electrocardiogram (ECG) – a shortening of the QT interval. It is caused by mutations in genes encoding ion channels that shorten the cardiac action potential, and appears to be inherited in an autosomal dominant pattern.[1] The condition is diagnosed using a 12-lead ECG.[2] Short QT syndrome can be treated using an implantable cardioverter-defibrillator or medications including quinidine.[3] Short QT syndrome was first described in 2000,[4] and the first genetic mutation associated with the condition was identified in 2004.[5]
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ShortQTsyndrome (SQT) is a very rare genetic disease of the electrical system of the heart, and is associated with an increased risk of abnormal heart...
Long QTsyndrome (LQTS) is a condition affecting repolarization (relaxing) of the heart after a heartbeat, giving rise to an abnormally lengthy QT interval...
in the QT interval can be caused by genetic conditions such as long QTsyndrome, by certain medications such as sotalol or pitolisant, by disturbances...
Look up QT, Qt, qt, or q.t. in Wiktionary, the free dictionary. QT or Qt may refer to: The Qt Company, a Finnish software developer QT Hotels & Resorts...
conduction defect (PCCD), early repolarization syndrome, mixed sodium channel disease, and shortQTsyndrome. In 20% of cases, no cause of death can be found...
disorder shortQTsyndrome. A number of clinically successful drugs in the market have had the tendency to inhibit hERG, lengthening the QT and potentially...
diarrhea, low serum magnesium, and low serum potassium or congenital long QTsyndrome. It can be seen in malnourished individuals and chronic alcoholics, due...
ventricular noncompaction Ion Channelopathies like the Long QTsyndrome and the very rare ShortQTsyndrome Catecholaminergic polymorphic ventricular tachycardia...
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There has also been an association between early repolarization and shortQTsyndrome. Male gender J-point and horizontal or descending / downsloping ST...
information to consider for differential diagnosis. Sinus tachycardia Long QTsyndrome Hafeez Y, Grossman SA (2020). "Sinus Bradycardia". StatPearls. Treasure...
Dressler syndrome is a secondary form of pericarditis that occurs in the setting of injury to the heart or the pericardium (the outer lining of the heart)...
a prolongation of the QT interval. QT prolongation may be congenital or acquired. Congenital problems include long QTsyndrome and catecholaminergic polymorphic...
arrhythmia syndromes include Long QTsyndrome (LQTS), Brugada Syndrome, Catecholaminergic polymorphic ventricular tachycardia, and ShortQTsyndrome. Many...
tachycardia-bradycardia syndrome Other presenting signs or symptoms can include confusion, fatigue, palpitations, chest pain, shortness of breath, headache...
Trifascicular block (LAFP plus FPFB plus RBBB) QTsyndromes Brugada syndromeShortQTsyndrome Long QTsyndromes, genetic and drug-induced Right and left atrial...
Atrioventricular reentrant tachycardia AV nodal reentrant tachycardia Brugada syndrome Circulatory shock and its various causes (obstructive shock, cardiogenic...
Causes of SADS in young people include viral myocarditis, long QTsyndrome, Brugada syndrome, Catecholaminergic polymorphic ventricular tachycardia, hypertrophic...
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