Phakomatosis pigmentovascularis | |
---|---|
Other names | Association of cutaneous vascular malformations and different pigmentary disorders[1] |
Specialty | Dermatology |
Phakomatosis pigmentovascularis is a rare neurocutanous condition where there is coexistence of a capillary malformation (port-wine stain) with various melanocytic lesions, including dermal melanocytosis (Mongolian spots), nevus spilus, and nevus of Ota.