Disorder affecting development of one side of the brain
Medical condition
Hemimegalencephaly
Left-sided hemimegalencephaly in a person with neurofibromatosis[1]
Specialty
Neurology, rheumatology
Symptoms
Frequent seizures often resistant to medicine
Usual onset
Congenital
Duration
Long term
Treatment
Hemispherectomy
Medication
Anti-epileptic drugs
Hemimegalencephaly (HME), or unilateral megalencephaly, is a rare congenital disorder affecting all or a part of a cerebral hemisphere.[2] It causes severe seizures, which are often frequent and hard to control. A minority might have seizure control with medicines, but most will need removal or disconnection of the affected hemisphere as the best chance. Uncontrolled, they often cause progressive intellectual disability and brain damage and stop development.[3]
^Acharya N, Reddy MS, Paulson CT, Prasanna D (January 2014). "Cranio-orbital-temporal neurofibromatosis: an uncommon subtype of neurofibromatosis type-1". Oman Journal of Ophthalmology. 7 (1): 43–5. doi:10.4103/0974-620X.127934. PMC 4008903. PMID 24799805.
^Sato, N; Yagishita, A; Oba, H; Miki, Y; Nakata, Y; Yamashita, F; Nemoto, K; Sugai, K; Sasaki, M (April 2007). "Hemimegalencephaly: a study of abnormalities occurring outside the involved hemisphere". AJNR. American Journal of Neuroradiology. 28 (4): 678–82. PMC 7977333. PMID 17416820.
^"Hemimegalencephaly - Why hemispherectomy is usually required". www.brainrecoveryproject.org. Retrieved 2018-04-12.
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