Acrokeratoelastoidosis of Costa | |
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Other names | Acrokeratoelastoidosis |
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Autosomal dominant is the inheritance manner for this condition | |
Specialty | Dermatology Genetics |
Usual onset | Childhood, adolescence, or early 20s.[1] |
Causes | Genetics |
Acrokeratoelastoidosis of Costa or Acrokeratoelastoidosis is a hereditary form of marginal keratoderma, and can be defined as a palmoplantar keratoderma. It is distinguished by tiny, firm pearly or warty papules on the sides of the hands and, occasionally, the feet. It is less common than the hereditary type of marginal keratoderma, keratoelastoidosis marginalis.[1]
Costa described acrokeratoelastoidosis in 1953, as a result, it is also known as Costa acrokeratoelastoidosis. Acrokeratoelastoidosis is a form of punctate palmoplantar keratoderma type 3 characterized by keratin and elastic tissue abnormalities.[1]
There have been autosomal dominant and sporadic forms observed. Acrokeratoelastoidosis isn't congenital; it develops gradually during puberty, or sometimes afterwards, and then stabilizes. In most cases, no treatment is required.[2]